<Entry>
<Accession>P30047</Accession>
        <ProteinName>GTP</ProteinName>
        <GeneName>GCHFR</GeneName>
        <OS_id>9606</OS_id>
        <ReferenceProteome>None</ReferenceProteome>
        <SubcellularLocation>
<Location>SL-0178</Location>
<Location>SL-0182</Location>
<Comments>Nucleus {ECO:0000269|PubMed:16778797}. Nucleus membrane {ECO:0000269|PubMed:16778797}. Cytoplasm, cytosol {ECO:0000269|PubMed:16778797}.</Comments>
</SubcellularLocation>
<CrossReferences>
<CrossReference>
<Database>UNIPROT</Database>
<ID>P30047</ID>
</CrossReference>
<CrossReference>
<Database>UNIPROT</Database>
<ID>B2R4L6</ID>
</CrossReference>
<CrossReference>
<Database>UNIPROT</Database>
<ID>B7ZLM8</ID>
</CrossReference>
<CrossReference>
<Database>UNIPROT</Database>
<ID>Q2M1Q2</ID>
</CrossReference>
<CrossReference>
<Database>UNIPROT</Database>
<ID>Q99749</ID>
</CrossReference>
<CrossReference>
<Database>PDB</Database>
<ID>6Z80</ID>
</CrossReference>
<CrossReference>
<Database>PDB</Database>
<ID>6Z85</ID>
</CrossReference>
<CrossReference>
<Database>PDB</Database>
<ID>7ACC</ID>
</CrossReference>
<CrossReference>
<Database>PDB</Database>
<ID>7AL9</ID>
</CrossReference>
<CrossReference>
<Database>PDB</Database>
<ID>7ALA</ID>
</CrossReference>
<CrossReference>
<Database>PDB</Database>
<ID>7ALB</ID>
</CrossReference>
<CrossReference>
<Database>PDB</Database>
<ID>7ALC</ID>
</CrossReference>
<CrossReference>
<Database>PDB</Database>
<ID>7ALQ</ID>
</CrossReference>
<CrossReference>
<Database>Pfam</Database>
<ID>PF06399</ID>
</CrossReference>
<CrossReference>
<Database>OMIM</Database>
<ID>602437</ID>
</CrossReference>
<CrossReference>
<Database>DisGeNET</Database>
<ID>2644</ID>
</CrossReference>
</CrossReferences>
<Function>Mediates tetrahydrobiopterin inhibition of GTP cyclohydrolase 1. This inhibition is reversed by L-phenylalanine. {ECO:0000269|PubMed:16778797}.</Function>
<Interactions>
<Interaction>
<Partner>O75147</Partner>
<IntAct>EBI-21786208</IntAct>
<Score>0.35</Score>
</Interaction>
<Interaction>
<Partner>P30793</Partner>
<IntAct>EBI-958378</IntAct>
<Score>0.37</Score>
</Interaction>
<Interaction>
<Partner>P20155</Partner>
<IntAct>EBI-21762493</IntAct>
<Score>0.35</Score>
</Interaction>
<Interaction>
<Partner>Q8N0Z8</Partner>
<IntAct>EBI-21786208</IntAct>
<Score>0.35</Score>
</Interaction>
<Interaction>
<Partner>Q9Y450</Partner>
<IntAct>EBI-21786208</IntAct>
<Score>0.35</Score>
</Interaction>
<Interaction>
<Partner>Q96RR4</Partner>
<IntAct>EBI-21786208</IntAct>
<Score>0.35</Score>
</Interaction>
<Interaction>
<Partner>Q7Z5L9</Partner>
<IntAct>EBI-21786208</IntAct>
<Score>0.35</Score>
</Interaction>
<Interaction>
<Partner>Q5JSL3</Partner>
<IntAct>EBI-21786208</IntAct>
<Score>0.35</Score>
</Interaction>
<Interaction>
<Partner>Q13951</Partner>
<IntAct>EBI-21786208</IntAct>
<Score>0.35</Score>
</Interaction>
<Interaction>
<Partner>Q04637</Partner>
<IntAct>EBI-21786208</IntAct>
<Score>0.35</Score>
</Interaction>
<Interaction>
<Partner>O76041</Partner>
<IntAct>EBI-21786208</IntAct>
<Score>0.35</Score>
</Interaction>
<Interaction>
<Partner>O00168</Partner>
<IntAct>EBI-21862664</IntAct>
<Score>0.35</Score>
</Interaction>
</Interactions>
<OntologyTerms>
<Ontology>GO:0005737</Ontology>
<Ontology>GO:0005829</Ontology>
<Ontology>GO:0030425</Ontology>
<Ontology>GO:0042470</Ontology>
<Ontology>GO:0031965</Ontology>
<Ontology>GO:0005654</Ontology>
<Ontology>GO:0005634</Ontology>
<Ontology>GO:0032991</Ontology>
<Ontology>GO:0016597</Ontology>
<Ontology>GO:0004857</Ontology>
<Ontology>GO:0044549</Ontology>
<Ontology>GO:0030742</Ontology>
<Ontology>GO:0044877</Ontology>
<Ontology>GO:0009890</Ontology>
<Ontology>GO:0043105</Ontology>
<Ontology>GO:0042133</Ontology>
<Ontology>GO:0006809</Ontology>
<Ontology>GO:0065003</Ontology>
</OntologyTerms>
<Topology>
        <Type>Unknown</Type>
        <Source>UniProt</Source>
        <Annotation>Sequence Analysis</Annotation>
        </Topology>
<Sequence>MPYLLISTQIRMEVGPTMVGDEQSDPELMQHLGASKRRALGNNFYEYYVDDPPRIVLDKLERRGFRVLSMTGVGQTLVWCLHKE</Sequence>
        <SequenceLength>84</SequenceLength>
        </Entry>